10.22376/ijpbs.2019.10.1.p1-12 Volume 6 Issue 4 2015 (October - December) Congenital lobar emphysema (CLE) is a clinico-radiological diagnosis, seen usually by four-six weeks of age (50% of patients) and rarely ( lessThan 5% of patients) after the age of six months. Here, we report a young male, a Known case of VSD presented with fever and cough with expectoration and physical examination revealing the features of right sided pneumothorax. X-ray chest, with subsequent CT-chest, lead to the diagnosis of CLE.. Patient is managed conservatively. DR.S.SAKTHI SELVA KUMAR M.D, DR.M.V.BHARGAVI, M.D AND PROF.DR.S.PALANIANDAVAN, M.D Congenital lobar emphysema, Ventricular septal defect. 830-835